‘Early myoclonic encephalopathy’ (ILAE; OMIM 609304) is one of the catastrophic epilepsies starting in the neonatal period. Prognosis is generally poor with early death in half of the patients. The ...
A 53 year-old woman developed a rapidly progressive dementia over three months associated with prominent myoclonic jerks. Over the following month, she became bed bound and mute. Creutzfeldt-Jakob ...
Sepsis-associated encephalopathy (SAE) is a diffuse brain dysfunction that occurs secondary to infection in the body without overt CNS infection. SAE is frequently encountered in critically ill ...